Ten years old girl was referred to our consultation for a tumefaction of the right buttock, it was soft consistency and mobile in relation to the deep planes (A). Magnetic resonance imaging reveals a large fatty lobulated mass well encapsulated with septa with low signal T1/T2 (B). Pathological examination of the resection piece confirmed the diagnosis of lipoblastoma (C). Lipoblastoma is a rare benign pediatric tumor derived from embryonic fat. It is often morphologically indistinguishable from primitive myxoid mesenchymal tumor of infancy. Translocations affecting the 8q11–13 region are commonly reported with lipoblastoma and proper diagnosis requires cytogenetic analysis to distinguish it from malignant myxoid liposarcoma. It is important to consider lipoblastoma in the diagnosis of a rapidly enlarging fatty mass in children. Complete resection is the only definitive treatment and should not be delayed when impingement on surrounding structures is imminent.

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Corresponding author
Zied Jlalia, Pediatric Orthopedics Department, Kassab Institute of Orthopedic Surgery, Ksar Said, Tunisia (jlalia.zied@gmail.com)