Bilateral maxillo-mandibular syngnathia in a newborn
Aziz El Madi, Youssef Bouabdallah
The Pan African Medical Journal. ;18:269. doi:10.11604/pamj..18.269.5071

Create an account  |  Sign in
PAMJ - Clinical Medicine PAMJ - Clinical Medicine
"Better health through knowledge sharing and information dissemination "

Images in clinical medicine

Bilateral maxillo-mandibular syngnathia in a newborn

Aziz El Madi, Youssef Bouabdallah
Pan Afr Med J. 2014; 18:269. doi:10.11604/pamj.2014.18.269.5071. Published 02 Aug 2014



The congenital fusion of the maxilla and mandible is a rare anomaly which is usually diagnosed after birth when it is discovered that the child is unable to open his mouth. Congenital synostosis of the mandible and maxilla is even less common than synechiae, with only 25 cases reported in the literature. We report the case of a five days-old newborn. History of the disease dates back to the birth by finding limiting the opening of the oral cavity with impossibility to breastfeed. The clinical examination of the child on admission to the neonatal department reveal a reactive newborn with birth weight at 2700 g, a good sucking reflex and limited mouth opening (A) with retrognathia (B). No signs of dehydration or malnutrition. Laboratory tests found urea at 1.62 g/l, creatinine at 15 mg/l. renal ultrasound found a right kidney measuring 3.7x 1.6 cm and the left 3.5 x 1.6 cm with well differentiated without dilatation of their pelvis. Maxillary CT with 3D reconstruction revealed hypoplasia of the ascending branches of the mandible; the temporomandibular joints were normal (C,D) with bilateral Maxillomandibular Syngnathia (E,F). A gastric tube was introduced for enteral feeding; the patient gained weight. After general anesthesia; tracheotomy, we proceeded by releasing synechiae between the dental arches and osteotomy of the bone bridge by endobuccal route. A prosthesis was put in place to keep the baby mouth open. The patient was admitted to intensive care where extubation was performed at J2; post-operative follow-up was uneventful.


Corresponding author:
Elmadi Aziz, Department of Pediatric Surgery I, Hassan II University Hospital, Fes 30000, Morocco
elmadichirped@yahoo.fr

©Aziz El Madi et al. This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/2.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.

More images in clinical medicine

 
 
 
 
 
 
 
 
    






PAMJ Images in Medicine and Public Health are archived on Pubmed Central. Access PAMJ archives on PMC here

Volume 34 (September - December 2019)

This image


Share this image:

Filter images [Reset filter]

By language

PAMJ is published in collaboration with the African Field Epidemiology Network (AFENET)
Currently tracked by: DOAJ, AIM, Google Scholar, AJOL, EBSCO, Scopus, Embase, IC, HINARI, Global Health, PubMed Central, PubMed/Medline, Ulrichsweb, More to come . Member of COPE.

ISSN: 1937-8688. © 2019 - Pan African Medical Journal. All rights reserved